AIEOP
Presentazione del nuovo Mod. 1.01
Bologna 02 marzo 2016
Transcodifica dei
codici diagnosi AIEOP
in ICD-O-3
Maria Luisa Mosso
Registro Tumori Infantili Piemonte
Mod 1.01
Codifica variabili riguardanti il tumore
• Morfologia
• Comportamento
• Topografia
ICD-O e ICCC
ICD-O-1
1976
Birch and Marsden 1987
Used in the IARC study “International Incidence of Childhood Cancer,” (IICC-1) Parkin et
al 1988
ICD-O-2
1990
ICCC-2
1996
Kramarova and Stiller Int. J. Cancer: 68,759-765 1996
ICD-O-3
2000
ICCC-3
2005
Steliarova-Foucher, Stiller, Lacour, Kaatsch Cancer 2005;103:1457–67.
ICD-O-3.1
2011 prima revisione
Morfologia: codifica Mod1.01
1000
LEUCEMIA
1500
LINFOMA
2000
TUMORI DEL SISTEMA NERVOSO CENTRALE
2500
TUMORI DEL SISTEMA NERVOSO SIMPATICO
3000
RETINOBLASTOMA
3500
TUMORI RENALI
4000
TUMORI EPATICI
4500
TUMORI OSSEI
5000
TUMORI GONADICI E TUMORI DELLE CELLULE GERMINALI
5500
TERATOMA MALIGNO E CARCINOMA EMBRIONARIO (NON GONADICO)
6000
TUMORI DEI TESSUTI MOLLI
6500
MELANOMA MALIGNO (NON SNC)
7000
TUMORI MISCELLANEI
8000
RETICOLOENDOTELIOSI
8300
MESOTELIOMA
8510
SINDROMI MIELODISPLASICHE
ICCC-3 International Classification of Childhood Cancer, Third Edition
I
Leukemias, myeloproliferative diseases, and myelodysplastic diseases
II
Lymphomas and reticuloendothelial neoplasm's
III
CNS and miscellaneous intracranial and intraspinal neoplasms
IV Neuroblastoma and other peripheral nervous cell tumors
V
Retinoblastoma
VI Renal tumors
VII Hepatic tumors
VIII Malignant bone tumors
IX Soft tissue and other extraosseous sarcomas
X Germ cell tumors, trophoblastic tumors, and neoplasms of gonads
XI Other malignant epithelial neoplasms and malignant melanomas
XII Other and unspecified malignant neoplasms
Classification of Childhood Cancer, third edition
Eva Steliarova-Foucher , Charles Stiller
Applica le regole, nomenclatura e codici (morfologia, topografia
e comportamento) dell’ICD-O-3.
Le categorie sono definite in conformità con le classificazioni
internazionali di patologia e genetica dei tumori, in particolare
con la serie della Classificazione Istologica Internazionale dei
Tumori dell’OMS, i cosiddetti Blue Books.
Anche se inserisce nuovi concetti di istogenesi tumorale,
garantisce la continuità con le precedenti classificazioni.
Sono stati sviluppati 3 livelli di classificazione gerarchica: il
Livello 1 (12 gruppi diagnostici principali) e il Livello 2 (47 sotto
gruppi diagnostici) comprende la tabella di classificazione
principale. Il Livello 3 è un’estensione opzionale della
classificazione.
Sono classificati in ICCC-3 solo i tumori con comportamento
maligno, con l’eccezione dei tumori endocranici e endorachidei.
L’uso di un sistema di
classificazione internazionale è
particolarmente importante nel
campo dell’oncologia pediatrica, in
cui la bassa frequenza di casi
richiede procedure rigorose per
garantire la comparabilità dei dati.
Steliarova-Foucher, Stiller, Lacour, Kaatsch
Cancer 2005;103:1457–67.
Distribuzione di tutti tumori per età in Italia
età 0-19
età 20+
ICD-O-3
International Classification of Diseases for Oncology
World Health Organization
• Sezione ‘topografia’= ICD-10
• Include nuovi termini, codici, sinonimi e cambiamenti di
comportamento dei Blue Books dell’OMS (2007- 2010).
• Codifica tutti i tumori e il loro comportamento
• ICD-O-3
Third edition of ICD-O (2000)
• ICD-O-3.1 ICD-O-3 First Revision (2011)
http://codes.iarc.fr
http://apps.who.int/bookorders/
Mod1.01 1972-2014
Morfologie: ricodifica in ICD-O-3
SI
Mod1.01
NO
TOTALE
ROT-CINECARTIP
Patologie specifiche
32987
-
-
32987
Categorie generiche
-
1093
3040
4133
Astrocitoma
-
533
1223
1756
Feocromocitoma
-
4
35
39
Istiocitosi
-
179
1586
1765
NB e ganglio NB
-
1122
1844
2966
32987
2931
7728
43646
76%
6%
18%
100%
Totale
Mod1.01
Tumori renali
Mod1.01
n
ICD-O-3 ICCC-3
3500
Tumori renali
29
3510
Tumore di Wilms
1592
8960/3
ICCC 6a
3520
Carcinoma a cellule chiare
66
8310/3
ICCC 6b
3530
Nefroma mesoblastico
71
8960/1
-
3540
Tumore rabdoide del rene
29
8963/3
ICCC 6a
3550
Sarcoma a cellule chiare
17
8964/3
ICCC 6a
3590
Tumori maligni renali, NAS
50
ICCC 6c
ICCC 6c
ICCC-3
VI. Renal tumors
a. Nephroblastoma and other nonepithelial renal tumors
8959/3 Malignant cystic nephroma
8960/3 Wilms tumor
8963/3 Rhabdoid sarcoma
8964/3 Clear cell sarcoma of kidney
9364/3 Peripheral primitive neuroectodermal tumor, NOS PPNET
b. Renal carcinomas
8010–8041, 8050–8075, 8082, 8120–8122, 8130–8141, 8143, 8155,
8190–8201, 8210, 8211, 8221–8231, 8240, 8241, 8244–8246,
8260–8263, 8290, 8310, 8320, 8323, 8401, 8430, 8440, 8480–8490, 8504, 8510, 8550, 8560–8576
8311, 8312, 8316–8319, 8361
c. Unspecified malignant renal tumors
….
ICD-O-3 online
morfologia
esempio: osteosarcoma condroblastico
Morphological Codes
ICD-O-3.1 (2011)
Select ICD-O code and name:
9180/3 Osteosarcoma, NOS
9181/3 Chondroblastic osteosarcoma
9182/3 Fibroblastic osteosarcoma
9183/3 Telangiectatic osteosarcoma
9184/3 Osteosarcoma in Paget disease of bone
9185/3 Small cell osteosarcoma
9186/3 Central osteosarcoma
9187/3 Intraosseous well differentiated osteosarcoma
9192/3 Parosteal osteosarcoma
9193/3 Periosteal osteosarcoma
9194/3 High grade surface osteosarcoma
9195/3 Intracortical osteosarcoma
OSTEOS
ICD-O-3 online
morfologia
9181/3 Chondroblastic osteosarcoma
Definitions
Bone ICD-O-3 topography code: C40-C41
ICD10: C40-C41
Chondroblastic osteosarcoma is a subtype of osteosarcoma, characterized by the
production of a chondroid matrix of variable cellularity, most commonly high grade
hyaline cartilage. Approximately 25% of osteosarcomas are chondroblastic
ICD-O-3 online
topografia
esempio: femore
…….
C39
OTHER AND ILL-DEFINED SITES WITHIN RESPIRATORY SYSTEM AMD INTRATHORACIC ORGANS
C40
BONES, JOINTS AND ARTICULAR CARTILAGE OF LIMBS
C40.0 Long bones of upper limb, scapula and associated joints
C40.1 Short bones of upper limb and associated joints
C40.2
Long bones of lower limb and associated joints
C40.3 Short bones of lower limb and associated joints
C40.8 Overlapping lesion of bones, joints and articular cartilage of limbs
C40.9 Bone of limb, NOS
C41
BONES, JOINTS AND ARTICULAR CARTILAGE OF OTHER AND UNSPECIFIED SITES
C41.0 Bones of skull and face and associated joints
C41.1 Mandible
C41.2 Vertebral column
C41.3 Rib, sternum, clavicle and associated joints
C41.4 Pelvic bones, sacrum, coccyx and associated joints
C41.8 Overlapping lesion of bones, joints and articular cartilage
C41.9 Bone, NOS
…….
ICD-O-3 online
morfologia
Esempio: tumore rabdoide maligno
Morphological Codes
ICD-O-3.1 (2011)
RHABDOID
Select ICD-O code name:
Select ICD-O code and name:
8014/3 Large cell carcinoma with rhabdoid phenotype
8963/3 Malignant rhabdoid tumor
9508/3 Atypical teratoid/rhabdoid tumor
9538/3 Rhabdoid meningioma
ICD-O-3 online
topografia
8963/3 Malignant rhabdoid tumor
Synonyms
Rhabdoid tumor, NOS
Rhabdoid sarcoma
Liver and intrahepatic bile ducts:
Prostate gland:
Connective, subcutaneous …
Kidney
C22
C61
C49
C64
ICCC3 9a
ICCC3 6a
ICD-O-3 online
morfologia
esempio: neuroblastoma
Morphological Codes
ICD-O-3.1 (2011)
Select ICD-O code name:
9490/3 Ganglioneuroblastoma
9500/3 Neuroblastoma, NOS
9504/3 Spongioneuroblastoma
9522/3 Olfactory neuroblastoma
NEUROBL
ICD-O-3 online
morfologia
9500/3 Neuroblastoma, NOS
Synonyms
Sympathicoblastoma
Central neuroblastoma
Definitions ….
Tumours of the central nervous system
C70, C71 and C72
ICD10: C71
Kidney
IC64
ICD10: C64
Prostate gland
C61
ICD10: C61
Peripheral nerves and autonomic nervous
system
C47
ICD10: C47
Adrenal gland
C74
ICD10: C74
ICCC3 04a
ICD-O-3 online
topografia
C47
C47.0
C47.1
C47.2
C47.3
C47.4
C47.5
C47.6
C47.8
C47.9
PERIPHERAL NERVES AND AUTONOMIC NERVOUS SYSTEM
head, face, and neck
upper limb and shoulder
lower limb and hip
thorax
abdomen
pelvis
trunk, NOS
Overlapping lesion
Autonomic nervous system, NOS
